How To Diagnose PAPVR & What Is The Best Medicine For It?

Your healthcare provider will perform diagnosis, usually, a physical exam based on your signs and symptoms.1

The diagnosis of the condition is often challenging and PAPVR was diagnosed based on CT imaging findings.2

The best treatment for PAPVR involves a heart operation to re-route all of the pulmonary venous to drain the oxygenated blood to the left atrium.3,4

How To Diagnose PAPVR?

The diagnosis of PAPVR is based on signs and symptoms. Your healthcare provider will perform diagnosis, usually, a physical exam based on your signs and symptoms. The doctor will check for the heart murmur using a stethoscope.

An echocardiogram is the best diagnosis for PAPVR, this uses ultrasound to produce images of the heart. Different types of diagnosis include

Cardiac Catheterization- This is a procedure to examine the condition of your heart. During this procedure, a catheter is inserted through the blood vessel to the heart to determine how well your heart is working. This is very effective to diagnose and treat several heart conditions.1

Cardiac Diagnostics And Kid-Friendly Imaging- Magnetic resonance imaging (MRI) is a kid-friendly imaging test that uses a magnetic field and radio waves that provides a complete range of primary and tertiary diagnostic imaging of the body’s organs and structures.

Fetal Diagnostics Procedure – Fetal diagnosis is performed in monitoring the health of the fetus of an expectant mother. The diagnosis of the condition is often challenging and PAPVR was diagnosed based on CT imaging findings. It produces a rapid and accurate diagnosis of fetal abnormalities.

A medical study was conducted on a 55-year-old patient who was experiencing episodes of light-headedness, neck pain, and diaphoresis. He had no past medical history and was diagnosed using an echocardiogram and monitored through a cardiac event monitor. The diagnosis showed no arrhythmias however the frequency of the symptoms increased with atrial fibrillation. Based on the symptoms, the doctor suggested surgery.2

What Is The Best Medicine For PAPVR?

If two of the veins are affected, the symptoms like shortness of breath are more common. The best treatment for PAPVR involves a heart operation to re-route all of the pulmonary venous to drain the oxygenated blood to the left atrium.

The surgery is typically performed under general anesthesia meaning you will not be conscious during the surgery. The physician makes a perpendicular slit in front of the chest opens the breastbone and uncovers the heart. The surgery timing is often dependent on the extent of the obstruction. The surgery is performed usually within six months after birth however if there are complications, it is operated on an urgent basis. Untreated conditions can result in death.

Some cases of the condition may require therapies before surgery to stabilize the condition. Treatment is done to lower the risk during surgery. Clinical studies demonstrate that surgery produces the best outcomes.3,4

Partial anomalous pulmonary venous return (PAPVR) is an uncommon cardiovascular disease and present at the time of birth. It occurs when one or more pulmonary vein is connected to the wrong part of the heart or originated from the wrong blood vessel.

When only one vein is affected, it will not cause symptoms however more than one vein is affected, it may result in pulmonary tension. Isolated partial anomalous pulmonary venous is usually associated with the atrial septal defect and is treated through surgery.

References:

  1. “Congenital Heart Disease in Adults.” Mayo Clinic, Mayo Foundation for Medical Education and Research, 14 May 2020, www.mayoclinic.org/diseases-conditions/partial-anomalous-pulmonary-venous-return/cdc-20385691.
  2. Sears, Edmund H, et al. “Partial Anomalous Pulmonary Venous Return Presenting with Adult-Onset Pulmonary Hypertension.” Pulmonary Circulation, Medknow Publications & Media Pvt Ltd, 2012, www.ncbi.nlm.nih.gov/pmc/articles/PMC3401879/.
  3. University of Wisconsin Hospitals and Clinics Authority. “Partial Anomalous Pulmonary Venous Return (PAPVR).” UW Health, www.uwhealth.org/heart-cardiovascular/partial-anomalous-pulmonary-venous-return-papvr/10968.
  4. “Anomalous Pulmonary Venous Return.” Anomalous Pulmonary Venous Return | CS Mott Children’s Hospital | Michigan Medicine, www.mottchildren.org/conditions-treatments/ped-heart/conditions/anomalous-pulmonary-venous-return.

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