A patient who suffers from Anderson-Fabry disease must follow a balanced diet, which excludes or limits the consumption of certain foods that are not beneficial. A hyposodic/hypoproteic and low in fats diet are advisable.
What Not To Eat When You Have Anderson’s Disease?
The hyposodic / hypoproteic diet consists of not using kitchen salt, so foods will be seasoned and cooked with olive oil, alcoholic and carbonated beverages are forbidden, as well as the intake of liquids should be limited.
Misadvised Foods (Due to its High Protein Content):
Cereals and Derivatives: dried peas, dried beans, chickpeas, soybeans.
Fruits: nuts, pine nuts without shell, almonds with shell, peanuts without shell.
Meat, Fish and Eggs:
Moderate Consumption of: Oysters, octopus, clams, chirlas, chanquete, mussels, eels, red mullet, chicken, pork chop, egg white, whole egg.
Prohibited – Mackerel, Norway lobster, lobster, snails, sea bream, crab, rooster, sole, sea bass, grouper, fresh salmon, fresh cod, hake, monkfish, squid, trout, prawns, sardines, and all canned food. Also pork loin, veal, smoked and sausages, leg of lamb, lamb ribs, quail, partridge, ox, chicken, horse, rabbit and hare, duck, yolk.
Dairy Products and Derivatives: Milk powder, sweetened condensed milk, curd, Emental cheese, Parmesan, Camembert, Roquefort, ball, Gruyere, Manchego.
Fats and Oils: butter.
Sugars: Industrial pastries.
If a strict low sodium diet is indicated, all seafood except oysters will be prohibited. Do not use ketchup or mustard (unless it does not contain salt).
Not Recommended Additives (they contain salt):
Disodium phosphate: Cereals, cheeses, butter, bottled beverages.
Monosodium glutamate: Products to increase taste, meats, condiments, pickles, sweet soups, confectionery.
Sodium alginate: Shortbreads, chocolate shakes.
Sodium benzoate: Fruit juices.
Sodium hydroxide: Canned peas.
Sodium propionate: Breads.
Sodium sulfite: Dried fruits, prepared vegetables for soup, salad.
Sodium pectinate: Syrups and coating for cakes, butter, sorbets, salad dressings, compotes and jellies.
Sodium caseinate: Shortbread and other frozen products.
Baking soda: Yeast, tomato soup, flour, sorbets and jams.
Spinach has high sodium content; it can be included as long as the rest of the menu ingredients are low in salt.
Be careful with:
-The jams and fruits in syrup (except homemade).
-Medications that contain sodium in its formula (effervescent tablets).
What is a Low Fat Diet?
A low-fat diet is a meal plan with a low fat content in general, unhealthy fat and cholesterol. You may need to follow a low-fat diet if you have difficulty digesting or absorbing fats. You may also need to follow this type of diet if you have high cholesterol. You can also increase the amount of fiber you eat to lower your cholesterol level.
Soluble fiber is a type of fiber that helps lower cholesterol levels.
What Do You Need To Know About The Different Types Of Fat In Food?
Limit unhealthy fats: A diet with a cholesterol content, saturated fats and trans fats can cause your cholesterol to rise to an unhealthy level. The risk of having heart disease increases when the cholesterol level is not within a healthy range.
Cholesterol: Limit your cholesterol intake to less than 200 mg per day. Cholesterol is found in meats, eggs and dairy products.
Saturated fats: Limit your saturated fat intake to less than 7% of your total daily calories. Saturated fats are found in butter, cheese, ice cream, whole milk and palm oil. Meats, such as beef, pork, chicken skin and processed meats are also saturated fats. Processed meats include sausages and mortadella.
Trans fats: Avoid the consumption of trans fats whenever possible. Trans fats are used in fried and bakery foods. Although some foods do not have trans-fat in the package, they may contain up to 0.5 grams of fat per serving.
Patients with Anderson-Fabry disease may have kidney-related effects, which may even lead to kidney failure, which warrants certain treatments, but in turn a hyposodic and/or hypoproteic diet (low in salt and protein, respectively) is indicated. Also, in those patients with gastrointestinal involvement, a balanced diet low in fats is recommended.